home
***
CD-ROM
|
disk
|
FTP
|
other
***
search
/
CD-ROM Today (UK) (Spanish) 15
/
CDRT.iso
/
dp
/
0390
/
03908.txt
< prev
next >
Wrap
Text File
|
1994-01-17
|
6KB
|
153 lines
$Unique_ID{BRK03908}
$Pretitle{}
$Title{Kluver-Bucy Syndrome}
$Subject{Kluver-Bucy Syndrome Bilateral Temporal Lobe Disorder Pick's Disease
Alzheimer's Disease Korsakoff's Syndrome }
$Volume{}
$Log{}
Copyright (C) 1992 National Organization for Rare Disorders, Inc.
872:
Kluver-Bucy Syndrome
** IMPORTANT **
It is possible that the main title of the article (Kluver-Bucy Syndrome)
is not the name you expected. Please check the SYNONYM listing to find the
alternate names and disorder subdivisions covered by this article.
Synonyms
Bilateral Temporal Lobe Disorder
Information on the following diseases can be found in the Related
Disorders section of this report:
Pick's Disease
Alzheimer's Disease
Korsakoff's Syndrome
General Discussion
** REMINDER **
The Information contained in the Rare Disease Database is provided for
educational purposes only. It should not be used for diagnostic or treatment
purposes. If you wish to obtain more information about this disorder, please
contact your personal physician and/or the agencies listed in the "Resources"
section of this report.
Kluver-Bucy Syndrome is a very rare cerebral neurological (brain
disorder. Major symptoms may include an urge to put all kinds of objects
into the mouth, memory loss, extreme sexual behavior, placidity, and visual
distractibility.
Symptoms
Kluver-Bucy Syndrome is characterized by loss of memory. There may also be
indiscriminate sexual behavior. However, other emotional behavior in
response to stimuli is usually lacking (indifference or placidity). An
almost uncontrollable appetite for food is also noted. There may also be
other forms of dementia (loss of reason) as well. There is an excessive
tendency to put all sorts of objects in the mouth, and easy extractability by
external stimuli (particularly visual) is usually present.
Causes
Kluver-Bucy Syndrome is the result of damage to the temporal lobes of the
brain. This may be the result of trauma to the brain itself, or the result
of other degenerative brain diseases, or it can be caused by some forms of
herpes simplex encephalitis (a viral brain infection).
Affected Population
Kluver-Bucy Syndrome is a very rare disease that affects males and females
equally.
Related Disorders
Symptoms of the following disorders can be similar to those of Kluver-Bucy
Syndrome. Comparisons may be useful for a differential diagnosis:
Pick's Disease is a very rare progressive neurological disease affecting
the lobes of the brain. Major symptoms may include changes in intellect,
behavior and personality. It is characterized by progressive deterioration
of intellect with changes in behavior and personality. The memory is usually
intact in the early stages of the disease and there is less disorientation
than in Alzheimer's Disease. However, in later stages there is loss of motor
control as well as confusion and severe dementia. (For more information on
this disorder, choose "Pick" as your search term in the Rare Disease
Database).
Alzheimer's Disease is a common progressive disorder of the brain
affecting memory, thought and language. Groups of nerve endings in the
cortex of the brains of people with Alzheimer's degenerates and disrupts the
passage of electrochemical signals between the cells. Affected individuals
become increasingly forgetful. As memory losses increase, personality, mood
and behavior also tend to change. Judgement, concentration, speech and
physical coordination may also be affected. (For more information on this
disorder, choose "Alzheimer" as your search term in the Rare Disease
Database).
Korsakoff's Syndrome is a deficiency of vitamin B-1 which causes
cardiovascular, central and peripheral nervous system disturbances. Early
symptoms of Korsakoff's syndrome include fatigue, irritation, poor memory,
difficulty sleeping, chest pain, abdominal discomfort, poor appetite and
constipation. Later symptoms are principally cardiovascular and
neurological. (For more information on this disorder, choose "Korsakoff" as
your search term in the Rare Disease Database).
Therapies: Standard
Treatment of Kluver-Bucy is symptomatic and supportive.
Therapies: Investigational
This disease entry is based upon medical information available through April
1992. Since NORD's resources are limited, it is not possible to keep every
entry in the Rare Disease Database completely current and accurate. Please
check with the agencies listed in the Resources section for the most current
information about this disorder.
Resources
For more information on Kluver-Bucy Syndrome, please contact:
National Organization for Rare Disorders (NORD)
P.O. Box 8923
New Fairfield, CT 06812-1783
(203) 746-6518
NIH/National Institute of Neurological Disorders & Stroke (NINDS)
9000 Rockville Pike
Bethesda, MD 20892
(301) 496-5751
(800) 352-9424
Alzheimer's Disease and Related Disorders Association, Inc.
National Headquarters
919 N. Michigan Ave., Suite 1000
Chicago, IL 60611
(312) 335-8700
(800) 272-3900
References
CECIL TEXTBOOK OF MEDICINE, 19th Ed.: James B. Wyngaarden, and Lloyd H.
Smith, Jr., Editors; W.B. Saunders Co., 1990. Pp. 2080-2087.
PRINCIPLES OF NEUROLOGY, 4th Ed.; Raymond D. Adams, M.D. and Maurice
Victor, M.D., Editors; McGraw-Hill Information Services Company, 1989. Pp.
360-363, 451-452.
THE MERCK MANUAL OF GERIATRICS, 1st Ed.; William B. Abrams, M.D. and
Robert Berkow, M.D., Editors; Merck Sharp & Dohme Research Laboratories,
Rahway, NJ, 1990. Pp. 946.
KLUVER-BUCY SYNDROME WITH SEVERE AMNESIA SECONDARY TO HERPES
ENCEPHALITIS, Conlon, P. et al.; Can J Psychiatry, November, 1988, (issue 33,
(8)). Pp. 754-756.
KLUVER-BUCY SYNDROME. A CASE REPORT., Fragassi, NA, et al.; Acta Neurol,
April, 1990, (issue 12 (2)). Pp. 138-142.